Dr.RAHUL MISTRY, M20058
Craniofacial fibrous dysplasia is benign slowly progressive disease where normal craniofacial bones are replaced by immature fibro-osseous tissue.
Method and material-35 year male with normal visual acuity and fundus finding presented with left axial proptosis. On further evaluation craniofacial fibrous dysplasia involving left orbit was diagnosed. Rest ocular functions normal including normal audiometry.
Result-Left frontal craniotomy followed by medial maxillectomy and ethmoidectomy was done with fronto medial osteotomy. In periodic follow-up there was regression of proptosis. Initially diplopia present in lateral gaze of left eye but subsequent follow-up resolved it. Seven months CT shows some fibrodysplastic growth on left medial canthus. Patient was adviced to maintain bone density by diet and exercise.
Conclusion-Early surgical intervention is needed to stop further progression. Periodic follow-up is recommended to monitor for recurrence and malignant transformation.
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